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Effect of VX-770 in Persons with Cystic Fibrosis and the G551D-CFTR Mutation FJ Accurso, SM Rowe, JP Clancy, MP Boyle, JM Dunitz, PR Durie, ... New England Journal of Medicine 363 (21), 1991-2003, 2010 | 944 | 2010 |
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Regulation of the epithelial sodium channel by serine proteases in human airways SH Donaldson, A Hirsh, DC Li, G Holloway, J Chao, RC Boucher, ... Journal of Biological Chemistry 277 (10), 8338-8345, 2002 | 333 | 2002 |
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Clinical effectiveness of elexacaftor/tezacaftor/ivacaftor in people with cystic fibrosis: a clinical trial DP Nichols, AC Paynter, SL Heltshe, SH Donaldson, CA Frederick, ... American journal of respiratory and critical care medicine 205 (5), 529-539, 2022 | 285 | 2022 |
Soluble mediators, not cilia, determine airway surface liquid volume in normal and cystic fibrosis superficial airway epithelia R Tarran, L Trout, SH Donaldson, RC Boucher The Journal of general physiology 127 (5), 591-604, 2006 | 258 | 2006 |
Cystic fibrosis lung disease starts in the small airways: can we treat it more effectively? HAWM Tiddens, SH Donaldson, M Rosenfeld, PD Paré Pediatric pulmonology 45 (2), 107-117, 2010 | 223 | 2010 |
Tezacaftor/Ivacaftor in Subjects with Cystic Fibrosis and F508del/F508del-CFTR or F508del/G551D-CFTR SH Donaldson, JM Pilewski, M Griese, J Cooke, L Viswanathan, E Tullis, ... American journal of respiratory and critical care medicine 197 (2), 214-224, 2018 | 220 | 2018 |
A biophysical basis for mucus solids concentration as a candidate biomarker for airways disease DB Hill, PA Vasquez, J Mellnik, SA McKinley, A Vose, F Mu, ... PloS one 9 (2), e87681, 2014 | 218 | 2014 |
Sodium channels and cystic fibrosis SH Donaldson, RC Boucher Chest 132 (5), 1631-1636, 2007 | 209 | 2007 |
SPLUNC1 regulates airway surface liquid volume by protecting ENaC from proteolytic cleavage A Garcia-Caballero, JE Rasmussen, E Gaillard, MJ Watson, JC Olsen, ... Proceedings of the national academy of sciences 106 (27), 11412-11417, 2009 | 199 | 2009 |
Update on pathogenesis of cystic fibrosis lung disease SH Donaldson, RC Boucher Current opinion in pulmonary medicine 9 (6), 486-491, 2003 | 191 | 2003 |
Basal nucleotide levels, release, and metabolism in normal and cystic fibrosis airways SH Donaldson, ER Lazarowski, M Picher, MR Knowles, MJ Stutts, ... Molecular Medicine 6, 969-982, 2000 | 122 | 2000 |
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